Advertisement
 

doctorslounge.com

 
Powered by
Careerbuilder

 

                    Home  |  Forums  |  Humor  |  Advertising  |  Contact
   Ask a Doctor

   News via RSS

   Newsletter

   Cardiology

   News

   Conferences

   CME

   Forum Archives

   Diseases

   Symptoms

   Labs

   Procedures

   Drugs

   Links
   Specialties

   Cardiology

   Dermatology

   Endocrinology

   Fertility

   Gastroenterology

   Gynecology

   Hematology

   Infections

   Nephrology

   Neurology

   Oncology

   Orthopedics

   Pediatrics

   Pharmacy

   Primary Care

   Psychiatry

   Pulmonology

   Rheumatology

   Surgery

   Urology

   Other Sections

   Membership

   Research Tools

   Medical Tutorials

   Medical Software

 

 Headlines:

 
 

Back to Cardiovascular Diseases

Tetralogy of Fallot

It is a congenital disease of the heart that is composed of several abnormalities. It is the commonest cyanotic heart disease.

1. Pulmonary stenosis (tight pulmonary valve). This leads to obstruction to the right ventricular outflow.

2. Ventricular septal defect (VSD)

3. The aorta is overriding the septum (straddle).

4. Right ventricular enlargement.

Hemodynamically the heart is one chamber.

Clinical suspicion

The severity of obstruction to right ventricular outflow is of fundamental significance. When the obstruction is severe, the pulmonary blood flow is reduced markedly, and a large volume of deoxygenated systemic venous blood is shunted from right to left across the ventricular septal defect. Severe cyanosis (blue coloration of the skin) and erythrocytosis occur, and symptoms and sequelae of decreased oxygen are prominent. In many infants and children the obstruction is mild but progressive.

Radiologic examination characteristically reveals a normal-sized, boot-shaped heart (coeur en sabot) with prominence of the right ventricle and a concavity in the region of the pulmonary conus. The pulmonary vascular markings are typically diminished, and the aortic arch and knob may be on the right side.

Diagnosis

1. Echocardiography: easily diagnosis the condition.

Treatment

1. Total surgical correction

Patients are usually diagnosed and treated during childhood. Total surgical correction is ideal.

The size of the pulmonary arteries rather than the age or size of the infant or child is the most important determinant in establishing candidacy for primary repair. Pronounced thinning of the pulmonary arteries is a relative contraindication for an early corrective surgical procedure.

2. Shunt procedure

When pronounced thinning of the pulmonary artery is present, a palliative operation, such as creation of a systemic arterial-pulmonary arterial shunt, is carried out and is usually followed by complete correction, which can be carried out at a lower risk later in childhood.

advertisement.gif (61x7 -- 0 bytes)
 

Are you a doctor or a nurse?

Do you want to join the Doctors Lounge online medical community?

Participate in editorial activities (publish, peer review, edit) and give a helping hand to the largest online community of patients.

Click on the link below to see the requirements:

Doctors Lounge Membership Application


previous.gif (72x17 -- 347 bytes) next.gif (72x17 -- 277 bytes)
 

 advertisement.gif (61x7 -- 0 bytes)

 

 



We subscribe to the HONcode principles of the HON Foundation. Click to verify.
We subscribe to the HONcode principles. Verify here

Privacy Statement | Terms & Conditions | Editorial Board | About us
Copyright 2001-2012 DoctorsLounge. All rights reserved.